Publisher's Synopsis
Monografiya posvyashchena etiologicheskim i patogeneticheskim aspektam manifestnykh i latentnykh narusheniy porfirinovogo obmena i ikh klinicheskim, biokhimicheskim i differentsial'no-diagnosticheskim priznakam. Obobshcheny otechestvennye i zarubezhnye dostizheniya za poslednie 25 let v oblasti issledovaniya porfirinovogo dismetabolizma. Predstavlena kontseptsiya ob etapnosti formirovaniya porfirinovogo dismetabolizma u bol'nykh s khronicheskimi diffuznymi zabolevaniyami pecheni, boleznyami serdechno-sosudistoy sistemy i drugimi patologicheskimi sostoyaniyami vnutrennikh organov. Otsenivaetsya vliyanie obmena porfirinov na techenie i prognoz razlichnykh zabolevaniy vnutrennikh organov. Izuchena rol' khronicheskikh HBV- i HCV-infektsiy v vozniknovenii rannikh i manifestnykh narusheniyakh porfirinovogo obmena. Shiroko predstavlena informatsiya po lecheniyu narusheniy obmena porfirinov, v tom chisle preparatami novykh pokoleniy (ursodezoksikholevaya kislota, al'fa-interferon i dr.), naznachenie kotorykh obosnovano pri porfirinovom dismetabolizme. Izdanie rasschitano na vrachey razlichnykh profiley: terapevtov, gastroenterologov, gepatologov, kardiologov, endokrinologov, gematologov, dermatologov, nevropatologov, profpatologov i drugikh spetsial'nostey.